DIET LOW IN SALT

Nutritional Approach for Phenylketonuria (PKU)

Phenylketonuria (PKU) is an inherited metabolic disorder affecting the body’s ability to process phenylalanine, an amino acid found in various proteins. Early diagnosis and implementing a low-phenylalanine diet are critical to preventing brain damage.

Essential Principles of a Low-Phenylalanine Diet:

• Include tyrosine supplementation while restricting phenylalanine intake.
• Consume only the necessary amount of phenylalanine for normal growth and bodily functions.
• Ensure sufficient protein and energy intake to support normal growth.
• Tailor the diet based on regular monitoring of blood phenylalanine levels.
• Commit to a lifelong adherence to the low-phenylalanine diet.

Foods to Incorporate and Avoid:

Include:

• Modified amino acid formula for newborns with minimal or no phenylalanine.
• Small amounts of certain foods with negligible phenylalanine content, such as sugar, jam, vegetable oil, and select fruits and vegetables.
• Controlled intake of bread, pasta, rice, and cereal.

Avoid:

• Chocolate, cheese, beans, milk, nuts, eggs, peas, fish, chicken, soybeans, meat.
• Products containing aspartame, such as diet sodas and artificial sweeteners.

Specialized Nutritional Products:

• Utilize specially formulated products with protein hydrolysates that have reduced phenylalanine content.
• These products provide essential vitamins, minerals, and proteins.

Guidance from Experts:

• Seek advice from healthcare professionals, including nutritionists and physicians.
• Regular consultations with specialists help adapt the diet to individual conditions and needs.

Note: This information serves as a general guide, and individuals with PKU should consult their healthcare team for personalized advice.