LOW-PHENYLALANINE DIET

Nutritional Approach for Phenylketonuria (PKU)

Phenylketonuria (PKU) is a hereditary metabolic disorder that affects the body’s ability to process phenylalanine, an amino acid found in various proteins. Early diagnosis and the implementation of a low-phenylalanine diet are crucial to prevent brain damage.

Key Principles of a Low-Phenylalanine Diet:

• Tyrosine supplementation is essential while restricting the intake of phenylalanine.
• The goal is to consume only the necessary amount of phenylalanine for normal growth and bodily functions.
• Ensure an adequate intake of protein and energy to support normal growth.
• Individualize the diet based on regular monitoring of blood phenylalanine levels.
• Lifelong commitment to the low-phenylalanine diet.

Foods to Include and Avoid:

Foods to Include:

• Modified amino acid formula for newborns with minimal or no phenylalanine.
• Small amounts of certain foods with negligible phenylalanine content, such as sugar, jam, vegetable oil, and select fruits and vegetables.
• Controlled intake of bread, pasta, rice, and cereal.

Foods to Avoid:

• Chocolate, cheese, beans, milk, nuts, eggs, peas, fish, chicken, soybeans, meat.
• Products containing aspartame, such as diet sodas and artificial sweeteners.

Special Nutritional Products:

• Utilize specially formulated products with protein hydrolysates that have reduced phenylalanine content.
• These products provide essential vitamins, minerals, and proteins.

Expert Guidance:

• Seek advice from healthcare professionals, including nutritionists and physicians.
• Regular consultations with specialists help adapt the diet to individual conditions and needs.

Note: This information is a general guide, and individuals with PKU should consult their healthcare team for personalized advice.